plasurВопросы реконструктивной и пластической хирургииIssues of Reconstructive and Plastic Surgery1814-1471АНО "НИИ микрохирургии"10.52581/1814-1471/89/05plasur-261Research ArticleВ ПОМОЩЬ ПРАКТИЧЕСКОМУ ВРАЧУAID TO THE PHISICIANВрожденный ложный сустав костей голени у детей. Роль микрохирургии в реконструкции конечностейCongenital pseudoarthrosis of the tibia in children. The role of microsurgery in limb reconstructionhttps://orcid.org/0000-0001-8948-9225ГранкинД. Ю.GrankinD. Yu.

Гранкин Денис Юрьевич – научный сотрудник, врач травматолог-ортопед отделения реконструктивной микрохи рургии и хирургии кисти.

196603, Санкт-Петербург, Пушкин, ул. Парковая, д. 64–68

Denis Yu. Grankin - research associate, the Department for Reconstructive Microsurgery and Hand Surgery.

64–68, Parkovaya st., Pushkin, St. Petersburg, 196603

grankin.md@gmail.comhttps://orcid.org/0000-0003-1319-8979ГолянаС. И.GolyanaS. I.

Голяна Сергей Иванович – канд. мед. наук, руководитель отделения реконструктивной микрохирургии и хирургии кисти.

196603, Санкт-Петербург, Пушкин, ул. Парковая, д. 64–68

Sergey I. Golyana - Cand. Med. sci., head of the Department for Reconstructive Microsurgery and Hand Surgery.

64–68, Parkovaya st., Pushkin, St. Petersburg, 196603

ser.golyana@yandex.ruhttps://orcid.org/0000-0001-6544-1657ЗахарьянЕ. А.ZakharyanE. A.

Захарьян Екатерина Анатольевна – канд. мед. наук, руководитель отдела координации и качества оказания помощи детскому населению Управления по взаимодействию с регионами.

196603, Санкт-Петербург, Пушкин, ул. Парковая, д. 64–68

Ekaterina A. Zakharyan - Cand. Med. sci., head of the Department for Coordination and Quality of Assistance to the Children's Population of the Department for Interaction with the Regions.

64–68, Parkovaya st., Pushkin, St. Petersburg, 196603

zax-2008@mail.ruhttps://orcid.org/0000-0001-7837-4676АвдейчикН. В.AvdeichikN. V.

Авдейчик Наталья Валерьевна – канд. мед. наук, врач травматолог-ортопед отделения реконструктивной микрохирургии и хирургии кисти.

196603, Санкт-Петербург, Пушкин, ул. Парковая, д. 64–68

Natalia V. Avdeichik - Cand. Med. sci., orthopedic surgeon, the Department for Reconstructive Microsurgery and Hand Surgery.

64–68, Parkovaya st., Pushkin, St. Petersburg, 196603

natali_avdeichik@mail.ruНациональный медицинский исследовательский центр детской травматологии и ортопедии им. Г.И. Турнера Минздрава РоссииРоссияH. Turner National Medical Research Centre for Children’s Orthopedics and Trauma SurgeryRussian Federation2024280720242724555Copyright © Гранкин Д.Ю., Голяна С.И., Захарьян Е.А., Авдейчик Н.В., 20242024Гранкин Д.Ю., Голяна С.И., Захарьян Е.А., Авдейчик Н.В.Grankin D.Y., Golyana S.I., Zakharyan E.A., Avdeichik N.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://plasur.elpub.ru/jour/article/view/261

Проведен анализ отечественных и зарубежных источников литературы на тему врожденного ложного сустава костей голени (ВЛСКГ) у детей. В первой части статьи освещены современные представления об этиологии и патогенезе, методах и сроках консервативного и оперативного лечения, возможных осложнениях при лечении ВЛСКГ у детей. Особое внимание уделено случаям псевдоартроза костей голени в сочетании с нейрофиброматозом 1-го типа. Описаны показания и возможные осложнения микрохирургического этапа – замещения обширного дефекта большеберцовой кости свободным кровоснабжаемым аутотрансплантатом малоберцовой кости. При описании клинического случая представлен результат лечения пациента с ВЛСКГ на фоне нейрофиброматоза 1-го типа, осложненного обширным дефектом большеберцовой кости.

The analysis of domestic and foreign literature sources on сongenital pseudoarthrosis of the tibia in children. First part of the article describes about etiology and pathogenesis, methods and timing of conservative and surgical treatment, complications in the treatment of сongenital pseudoarthrosis of the tibia in children. Special attention is paid to cases of сongenital pseudoarthrosis of the tibia in combination with neurofibromatosis type 1. Indications and possible complications of the microsurgical stage – replacement of an extensive tibial defect with a free bloodsupplied fibular bone flap. The section description of the clinical case presents the result of treatment of a pediatric patient with сongenital pseudoarthrosis of the tibia against the background of neurofibromatosis type 1, complicated by an extensive defect of the tibia.

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The authors declare that there are no conflicts of interest present.